Ectodermal Dysplasia
case report
DOI:
https://doi.org/10.7308/aodontol/2012.48.11.07Keywords:
Ectodermal dysplasia, Anodontia, AdolescentAbstract
Ectodermal dysplasia includes a large and heterogeneous group of hereditary diseases characterized by clinical manifestations related to alterations in ectodermal structures, mainly hair, nails, teeth, and skin. The present study describes a clinical case of an eleven-year-old male patient that sought out dental services at a dentistry clinic in a higher education institution in Belo Horizonte, Brazil. The patient presented characteristics of ectodermic dysplasia, in hypohidrotic form, and a medical record of a number of members of the maternal family who had also been affected. A literature review and a discussion concerning the etiology and treatment for the described case was also carried out.
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References
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